Drug Description in Trials / DrugBank / KEGG DRUG


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No. 薬物名(臨床試験情報から抽出) DrugBank KEGG DRUG KEGG GENES KEGG PATHWAY 指定難病告示番号
164CuCl2----1件: 171 💬
2900mg TETA 4HCl Cuprior®----1件: 171 💬
3900mg TETA 4HCl Once Daily Formulation----1件: 171 💬
4[64Cu]Cl2----1件: 171 💬
5Acetate1件: Acetate---52件: 1, 2, 6, 10, 11, 13, 22, 35, 40, 46, 49, 51, 60, 63, 64, 65, 66, 67, 70, 71, 73, 75, 76, 77, 78, 79, 81, 83, 85, 86, 88, 89, 90, 96, 97, 113, 145, 156, 158, 162, 171, 206, 222, 223, 224, 225, 227, 235, 251, 265, 298, 299 💬
6Adeno-associated viral vector serotype 3B encoding shortened human ATP7B----1件: 171 💬
7Adeno-associated viral vector serotype 9 encoding human ATP7B----1件: 171 💬
8ALXN1840----1件: 171 💬
9Artamin 150 mg----1件: 171 💬
10Artamin 250 mg----1件: 171 💬
11BIS-CHOLINE TETRATHIOMOLYBDATE2件: Choline,
Tetrathiomolybdate
1件: Choline 💬 --1件: 171 💬
12BIS-CHOLINE TETRATHIOMOLYBDATE, bis[(2-Hydroxyethyl)trimethylammonium] tetrathiomolybdate2件: Choline,
Tetrathiomolybdate
1件: Choline 💬 --1件: 171 💬
13BOTULINUM TOXIN TYPE A1件: Botulinum toxin type A4件: Botulinum toxin type A ,
OnabotulinumtoxinA ,
AbobotulinumtoxinA ,
Incobotulinumtoxin A 💬
1件: SNAP25 💬 2件: Insulin secretion, Synaptic vesicle cycle 💬13件: 2, 5, 6, 7, 13, 15, 17, 47, 70, 113, 149, 171, 226 💬
14Bupropion1件: Bupropion3件: Bupropion hydrochloride ,
Bupropion ,
Bupropion hydrobromide 💬
2件: SLC6A2,
SLC6A3 💬
8件: Alcoholism, Amphetamine addiction, Cocaine addiction, Dopaminergic synapse, Neuroactive ligand signaling, Parkinson disease, Pathways of neurodegeneration - multiple diseases, Synaptic vesicle cycle 💬7件: 8, 18, 21, 96, 97, 171, 298 💬
15Bupropion Hydrochloride1件: Bupropion3件: Bupropion hydrochloride ,
Bupropion ,
Bupropion hydrobromide 💬
2件: SLC6A2,
SLC6A3 💬
8件: Alcoholism, Amphetamine addiction, Cocaine addiction, Dopaminergic synapse, Neuroactive ligand signaling, Parkinson disease, Pathways of neurodegeneration - multiple diseases, Synaptic vesicle cycle 💬1件: 171 💬
16CELECOXIB1件: Celecoxib1件: Celecoxib 💬 1件: PTGS2 💬 22件: Alzheimer disease, Arachidonic acid metabolism, C-type lectin receptor signaling pathway, Chemical carcinogenesis - DNA adducts, Efferocytosis, Human cytomegalovirus infection, Human papillomavirus infection, IL-17 signaling pathway, Kaposi sarcoma-associated herpesvirus infection, Leishmaniasis, MicroRNAs in cancer, NF-kappa B signaling pathway, Ovarian steroidogenesis, Oxytocin signaling pathway, Pathways in cancer, Pathways of neurodegeneration - multiple diseases, Regulation of lipolysis in adipocytes, Retrograde endocannabinoid signaling, Serotonergic synapse, Small cell lung cancer, TNF signaling pathway, VEGF signaling pathway 💬14件: 2, 3, 6, 13, 34, 46, 70, 89, 96, 97, 107, 161, 171, 271 💬
17Choline1件: Choline1件: Choline 💬 --4件: 93, 171, 193, 299 💬
18Copper1件: Copper---4件: 2, 169, 170, 171 💬
19COPPER (64CU) CHLORIDE1件: Copper---1件: 171 💬
20Cufence----2件: 58, 171 💬
21Cufence (trientine dihydrochloride)1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
22Cuprior----1件: 171 💬
23Cuprior 150 mg----1件: 171 💬
24Cuprior 150 mg film-coated tablets----1件: 171 💬
25Cuprior 150mg film-coated tablets----1件: 171 💬
26D-Penicillamine1件: Penicillamine1件: Penicillamine 💬 --1件: 171 💬
27D-penicillamine 150mg1件: Penicillamine1件: Penicillamine 💬 --1件: 171 💬
28D-penicillamine 250 mg1件: Penicillamine1件: Penicillamine 💬 --1件: 171 💬
29DEXMEDETOMIDINE1件: Dexmedetomidine2件: Dexmedetomidine ,
Dexmedetomidine hydrochloride 💬
3件: ADRA2A,
ADRA2B,
ADRA2C 💬
4件: Hormone signaling, Neuroactive ligand signaling, Neuroactive ligand-receptor interaction, cGMP-PKG signaling pathway 💬15件: 2, 4, 6, 21, 22, 34, 46, 70, 107, 113, 171, 212, 215, 226, 280 💬
30Diagnostic Test: 24 hour copper in urine and liver function test1件: Copper---1件: 171 💬
31Diagnostic Test: Imaging and fluid biomarkers----1件: 171 💬
32Diagnostic Test: urine and blood test----1件: 171 💬
33DMPS----1件: 171 💬
34DMSA----1件: 171 💬
35Fibroscan----1件: 171 💬
36Functional hepatic nitrogen clearance1件: Nitrogen1件: Nitrogen 💬 --1件: 171 💬
37Galactose1件: Galactose1件: Galactose 💬 --4件: 66, 171, 222, 257 💬
38Gandouling----1件: 171 💬
39Genetic: allogeneic mesenchymal stem cell transplantation----1件: 171 💬
40Genetic: GC310----1件: 171 💬
41Genetic: genetic test----1件: 171 💬
42Genetic: LY-M003----1件: 171 💬
43Genetic: LY-M003 Injection----1件: 171 💬
44Genetic: MWAV201----1件: 171 💬
45Genetic: Next generation sequencing----1件: 171 💬
46Genetic: UX7011件: UX701---1件: 171 💬
47Genetic: VTX-8011件: VTX-801---1件: 171 💬
48Gold1件: Gold---71件: 2, 5, 6, 11, 13, 17, 19, 21, 22, 28, 34, 35, 46, 49, 50, 53, 54, 56, 57, 58, 60, 63, 64, 65, 66, 68, 71, 75, 76, 77, 79, 84, 85, 86, 88, 91, 93, 95, 96, 97, 98, 107, 113, 127, 137, 158, 162, 167, 171, 193, 206, 215, 218, 222, 223, 224, 226, 227, 228, 230, 235, 271, 291, 294, 296, 298, 299, 310, 318, 331, 340 💬
49Group 1: DSL101 Low dose----1件: 171 💬
50Group 2: DSL101 Medium dose----1件: 171 💬
51Group 3: DSL101 High dose----1件: 171 💬
52Liver biopsy----3件: 171, 231, 240 💬
53Low copper diet1件: Copper---1件: 171 💬
54Metalcaptase----1件: 171 💬
55Metalcaptase® 150 mg gastro-resistant tablet----1件: 171 💬
56Metalcaptase® 300 mg gastro-resistant tablet----1件: 171 💬
57New TETA 4HCl Formulation----1件: 171 💬
58Nitrogen1件: Nitrogen1件: Nitrogen 💬 --6件: 5, 6, 17, 171, 211, 299 💬
59None----14件: 13, 46, 65, 84, 85, 96, 97, 106, 160, 161, 171, 222, 223, 299 💬
60NPC-02----1件: 171 💬
61Once a day Trientine----1件: 171 💬
62Other: Standard medical treatment----6件: 13, 96, 97, 149, 153, 171 💬
63PEMINE - 150 MG CAPSULE RIGIDE 50 CAPSULE----1件: 171 💬
64Penicillamine1件: Penicillamine1件: Penicillamine 💬 --2件: 51, 171 💬
65Penicillamine (D1-W12)1件: Penicillamine1件: Penicillamine 💬 --1件: 171 💬
66Penicillamine (W12-W60)1件: Penicillamine1件: Penicillamine 💬 --1件: 171 💬
67Plasma exchange----7件: 13, 43, 44, 64, 95, 171, 222 💬
68SoC Therapy----1件: 171 💬
69Standard of Care----18件: 6, 13, 49, 51, 57, 58, 63, 64, 79, 84, 96, 97, 113, 171, 223, 228, 240, 291 💬
70Standard of Care (SOC)----5件: 43, 44, 49, 85, 171 💬
71Standard of Care Medications----1件: 171 💬
72TETA 4HCl1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
73TETA 4HCL (60-----1件: 171 💬
74TETA 4HCL (W12-60)----1件: 171 💬
75TETA 4HCl formulation----1件: 171 💬
76TETA.4HCI1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
77TETA.4HCl1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
78Tetrathiomolybdate1件: Tetrathiomolybdate---3件: 85, 93, 171 💬
79Tiomolibdic acid----1件: 171 💬
80Trientine----2件: 58, 171 💬
81Trientine Dihydrochloride----2件: 58, 171 💬
82Trientine dihydrochloride 300mg capsules----1件: 171 💬
83Trientine tetrahydrochloride1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
84Triethylenetetramine1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
85Triethylenetetramine dihydrochloride1件: Triethylenetetramine2件: Trientine hydrochloride ,
Trientine tetrahydrochloride 💬
--1件: 171 💬
86Ultrasound----1件: 171 💬
87UX7011件: UX701---1件: 171 💬
88UX701 (1.0 × 10^13 genome copies/kg)1件: UX701---1件: 171 💬
89UX701 (2.0 × 10^13 genome copies/kg)1件: UX701---1件: 171 💬
90UX701 (5.0 × 10^12 genome copies/kg)1件: UX701---1件: 171 💬
91VTX-8011件: VTX-801---1件: 171 💬
92Wilzin----1件: 171 💬
93WTX101----1件: 171 💬
94Zinc1件: Zinc---7件: 2, 56, 85, 171, 222, 223, 299 💬
95Zinc acetate3件: Acetate,
Zinc,
Zinc acetate
1件: Zinc acetate 💬 --2件: 171, 299 💬
96ZINC ACETATE DIHYDRATE2件: Acetate,
Zinc acetate
1件: Zinc acetate 💬 --1件: 171 💬
97Zinc gluconate2件: Zinc,
Zinc gluconate
1件: Zinc gluconate 💬 --2件: 56, 171 💬
98Zink Natur-Drogeriet----1件: 171 💬