| 1 | 15N ammonium chloride (15NH4Cl) | [2] Ammonium chloride Ammonium chloride, Chloride ion | [1] D01139
D01139
| - | - | [1] 251 251 |
| 2 | 4-phenylbutyrate | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [2] 251 251, 299 |
| 3 | Acetohydroxamic Acid | [1] Acetohydroxamic acid Acetohydroxamic acid | [1] D00220
D00220
| - | - | [1] 251 251 |
| 4 | Acetohydroxamic Acid Oral Tablet [Lithostat] | [1] Acetohydroxamic acid Acetohydroxamic acid | [1] D00220
D00220
| - | - | [1] 251 251 |
| 5 | Alanine | [1] Alanine Alanine | [1] D00012
D00012
| - | - | [5] 6 6, 13, 251, 298, 299 |
| 6 | ALLOGENIC HUMAN HETEROLOGOUS LIVER CELLS | - | - | - | - | [1] 251 251 |
| 7 | Ammonium (15N) chloride | [1] Chloride ion Chloride ion | - | - | - | [1] 251 251 |
| 8 | Ammonium chloride | [2] Ammonium chloride Ammonium chloride, Chloride ion | [1] D01139
D01139
| - | - | [3] 96 96, 107, 251 |
| 9 | ARCT-810 | - | - | - | - | [1] 251 251 |
| 10 | Arginine | [1] Arginine Arginine | [1] D02982
D02982
| - | - | [11] 46 46, 58, 67, 78, 96, 97, 98, 113, 210, 251, 299 |
| 11 | ASA | - | - | - | - | [4] 13 13, 96, 97, 251 |
| 12 | Behavioral: Protein and calorie controlled diet | - | - | - | - | [1] 251 251 |
| 13 | Carglumic Acid | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [3] 245 245, 246, 251 |
| 14 | Celulas hepatocitos troncales adultas alogenicas de higado expandidas | - | - | - | - | [1] 251 251 |
| 15 | Chloride | [1] Chloride ion Chloride ion | - | - | - | [29] 6 6, 11, 13, 14, 34, 46, 50, 51, 53, 60, 65, 67, 78, 96, 97, 107, 127, 168, 171, 193, 227, 228, 251, 271, 288, 296, 297, 299, 338 |
| 16 | DTX301 | - | - | - | - | [1] 251 251 |
| 17 | Genetic: Ornithine transcarbamylase vector | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
| 18 | Genetic: recombinant adenovirus containing the ornithine transcarbamylase gene | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
| 19 | Genetic: scAAV8OTC | - | - | - | - | [1] 251 251 |
| 20 | Glyceryl tri-(4-phenylbutyrate) | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [1] 251 251 |
| 21 | Glyceryl tri-(4-phenylbutyrate)(GT4P) | [2] Glycerol phenylbutyrate Glycerol phenylbutyrate, Phenylbutyric acid | [1] D10127
D10127
| - | - | [1] 251 251 |
| 22 | GT4P | [1] Glycerol phenylbutyrate Glycerol phenylbutyrate | [1] D10127
D10127
| - | - | [1] 251 251 |
| 23 | Heparesc | - | - | - | - | [1] 251 251 |
| 24 | HepaStem | - | - | - | - | [1] 251 251 |
| 25 | HepaStem Infusion | - | - | - | - | [1] 251 251 |
| 26 | Heterologous Human Adult Liver-derived Progenitor Cells | - | - | - | - | [1] 251 251 |
| 27 | Heterologous Human Adult Liver-derived Progenitor Cells (HHALPC) | - | - | - | - | [1] 251 251 |
| 28 | HHALPC | - | - | - | - | [1] 251 251 |
| 29 | HHLivC | - | - | - | - | [1] 251 251 |
| 30 | HPN-100 | - | - | - | - | [1] 251 251 |
| 31 | Human Heterologous Liver Cells | - | - | - | - | [1] 251 251 |
| 32 | Human heterologous liver cells (for infusion) | - | - | - | - | [1] 251 251 |
| 33 | Isotopic Intravenous [13C]-Urea | [1] Urea Urea | [2] D00023
D00023
,
D01749
| - | - | [1] 251 251 |
| 34 | KB195 | - | - | - | - | [1] 251 251 |
| 35 | MRNA encoding modified Ornithine transcarbamylase | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
| 36 | MRT5201 | - | - | - | - | [1] 251 251 |
| 37 | NaPBA | - | - | - | - | [1] 251 251 |
| 38 | Neo-ASA | - | - | - | - | [1] 251 251 |
| 39 | Nitric Oxide | [1] Nitric Oxide Nitric Oxide | [1] D00074
D00074
| - | - | [8] 46 46, 85, 86, 98, 210, 251, 294, 299 |
| 40 | Nitric oxide supplement | [1] Nitric Oxide Nitric Oxide | [1] D00074
D00074
| - | - | [1] 251 251 |
| 41 | Oral prednisone | [1] Prednisone Prednisone | [1] D00473
D00473
| [1] NR3C1 NR3C1 💬 | [1] Neuroactive ligand-receptor interaction Neuroactive ligand-receptor interaction 💬 | [1] 251 251 |
| 42 | Ornithine | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [2] 245 245, 251 |
| 43 | Other: Aminoacid, alanine-infusion | [1] Alanine Alanine | [1] D00012
D00012
| - | - | [1] 251 251 |
| 44 | PHENYLBUTYRATE | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [12] 2 2, 3, 6, 8, 15, 93, 94, 244, 251, 297, 299, 338 |
| 45 | Prednisone | [1] Prednisone Prednisone | [1] D00473
D00473
| [1] NR3C1 NR3C1 💬 | [1] Neuroactive ligand-receptor interaction Neuroactive ligand-receptor interaction 💬 | [48] 2 2, 6, 11, 13, 14, 19, 26, 35, 40, 41, 42, 43, 44, 45, 46, 49, 50, 51, 53, 61, 63, 64, 65, 66, 79, 81, 84, 85, 86, 95, 96, 97, 113, 127, 162, 164, 205, 222, 224, 228, 251, 283, 284, 285, 288, 299, 300, 331 |
| 46 | Promethera HepaStem | - | - | - | - | [1] 251 251 |
| 47 | RAVICTI | [1] Glycerol phenylbutyrate Glycerol phenylbutyrate | [1] D10127
D10127
| - | - | [2] 251 251, 299 |
| 48 | Sodium phenylbutyrate | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [4] 2 2, 3, 8, 251 |
| 49 | SYNB1020 | - | - | - | - | [1] 251 251 |
| 50 | Urea | [1] Urea Urea | [2] D00023
D00023
,
D01749
| - | - | [2] 72 72, 251 |